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au.\*:("BONKOWSKY HL")

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ASSAY OF DELTA -AMINOLEVULINIC ACID SYNTHETASE IN HOMOGENATES OF MOUSE, RAT, AND HUMAN LIVER: SPECIES DIFFERENCES IN REQUIREMENT FOR AN EXOGENOUS SUCCINYL-COA-GENERATING SYSTEMBONKOWSKY HL; POMEROY JS.1978; ANAL. BIOCHEM.; USA; DA. 1978; VOL. 91; NO 1; PP. 82-91; BIBL. 24 REF.Article

HUMAN HEPATIC DELTA -AMINOLAEVULINATE SYNTHASE: REQUIREMENT OF AN EXOGENOUS SYSTEM FOR SUCCINYL-COENZYME A GENERATION TO DEMONSTRATE INCREASED ACTIVITY IN CIRRHOTIC AND ANTICONVULSANT-TREATED SUBJECTS.BONKOWSKY HL; POMEROY JS.1977; CLIN. SCI. MOLEC. MED.; G.B.; DA. 1977; VOL. 52; NO 5; PP. 509-521; BIBL. 1 P. 1/2Article

CHRONIC HEPATIC INFLAMMATION AND FIBROSIS DUE TO LOW DOSES OF PARACETAMOL.BONKOWSKY HL; MUDGE GH; MCMURTRY RJ et al.1978; LANCET; G.B.; DA. 1978; NO 8072; PP. 1016-1018; BIBL. 16 REF.Article

HEME SYNTHETASE DEFICIENCY IN HUMAN PROTOPORPHYRIA. DEMONSTRATION OF THE DEFECT IN LIVER AND CULTURED SKIN FIBROBLASTS. = DEFICIT EN HEME SYNTHETASE DANS LA PROTOPORPHYRIE HUMAINE. DEMONSTRATION DE L'ANOMALIE AU NIVEAU DU FOIE ET DANS LES FIBROBLASTES CUTANES EN CULTUREBONKOWSKY HL; BLOOMER JR; MAHONEY MJ et al.1975; J. CLIN. INVEST.; U.S.A.; DA. 1975; VOL. 56; NO 5; PP. 1139-1148; BIBL. 42 REF.Article

EVIDENCE FOR MULTIPLE SITES OF REGULATION OF HEME SYNTHESIS IN MURINE ERYTHROLEUKEMIA CELLSEBERT PS; BONKOWSKY HL; DEISSEROTH A et al.1979; J. NATION. CANCER INST.; USA; DA. 1979; VOL. 62; NO 5; PP. 1247-1250; BIBL. 24 REF.Article

HEPATIC HEME METABOLISM AND ITS CONTROLBONKOWSKY HL; SINCLAIR PR; SINCLAIR JF et al.1979; YALE J. BIOL. MED.; USA; DA. 1979; VOL. 52; NO 1; PP. 13-37; BIBL. 128 REF.Article

HEPATIC CYTOCHROME P-450 IN CHRONICALLY HYPOXEMIC RATSOU LC; HEALEY J; BONKOWSKY HL et al.1980; BIOCHEM. BIOPHYS. RES. COMMUN.; ISSN 0006-291X; USA; DA. 1980; VOL. 96; NO 3; PP. 1128-1134; BIBL. 26 REF.Article

STIMULATION OF HEMOGLOBIN SYNTHESIS IN MURINE ERYTHROLEUKEMIA CELLS BY LOW MOLECULAR WEIGHT KETONES, ALDEHYDES, ACIDS, ALCOHOLS AND ETHERSEBERT PS; BONKOWSKY HL; WARS I et al.1981; CHEM.-BIOL. INTERACT.; ISSN 0009-2797; NLD; DA. 1981; VOL. 36; NO 1; PP. 61-69; BIBL. 32 REF.Article

THE DIAGNOSIS OF ACUTE INTERMITTENT PORPHYRIA. USEFULNESS AND LIMITATIONS OF THE ERYTHROCYTE UROPORPHYRINOGEN 1 SYNTHASE ASSAYBOTTOMLEY SS; BONKOWSKY HL; KREIMER BIRNBAUM M et al.1981; AM. J. CLIN. PATHOL.; ISSN 0002-9173; USA; DA. 1981; VOL. 76; NO 2; PP. 133-139; BIBL. 33 REF.Article

METABOLISM OF HEPATIC HAEM AND "GREEN PIGMENTS" IN RATS GIVEN 2-ALLYL-2-ISOPROPYLACETAMIDE AND FERRIC CITRATE. A NEW MODEL FOR HEPATIC HAEM TURNOVERBONKOWSKY HL; HEALEY JF; SINCLAIR PR et al.1980; BIOCHEM. J.; GBR; DA. 1980; VOL. 188; NO 2; PP. 289-295; BIBL. 30 REF.Article

SEIZURE MANAGEMENT IN ACUTE HEPATIC PORPHYRIA: RISKS OF VALPROATE AND CLONAZEPAMBONKOWSKY HL; SINCLAIR PR; EMERY S et al.1980; NEUROLOGY; USA; DA. 1980; VOL. 30; NO 6; PP. 588-592; BIBL. 25 REF.Article

DECREASE IN HEPATIC CYTOCHROME P-450 BY COBALT. EVIDENCE FOR A ROLE OF COBALT PROTOPORPHYRINSINCLAIR JF; SINCLAIR PR; HEALEY JF et al.1982; BIOCHEM. J. (LOND.); ISSN 0006-2936; GBR; DA. 1982; VOL. 204; NO 1; PP. 103-109; BIBL. 35 REF.Article

IRON AND THE LIVER: ACUTE AND LONG-TERM EFFECTS OF IRON-LOADING ON HEPATIC HAEM METABOLISMBONKOWSKY HL; HEALEY JF; SINCLAIR PR et al.1981; BIOCHEM. J. (LOND.); ISSN 0006-2936; GBR; DA. 1981; VOL. 196; NO 1; PP. 57-64; BIBL. 40 REF.Article

INHERITANCE IN PROTOPORPHYRIA COMPARISON OF HAEM SYNTHETASE ACTIVITY IN SKIN FIBROBLASTS WITH CLINICAL FEATURES.BLOOMER JR; BONKOWSKY HL; EBERT PS et al.1976; LANCET; G.B.; DA. 1976; NO 7979; PP. 226-228; BIBL. 25 REF.Article

PORPHYRIN SYNTHESIS AND MITOCHONDRIAL RESPIRATION IN ACUTE INTERMITTENT PORPHYRIA: STUDIES USING CULTURED HUMAN FIBROBLASTS = SYNTHESE DES PORPHYRINES ET RESPIRATION DES MITOCHONDRIES DANS LA PORPHYRIE INTERMITTENTE AIGUE: ETUDE A L'AIDE DE FIBROBLASTES HUMAINS CULTIVESBONKOWSKY HL; TSCHUDY DP; WEINBACH EC et al.1975; J. LAB. CLIN. MED.; U.S.A.; DA. 1975; VOL. 85; NO 1; PP. 93-102; BIBL. 1P.1/2Article

COMPARATIVE EFFECTS OF GLYCEROL AND DEXTROSE ON PROPHYRIN PRECURSOR EXCRETION IN ACUTE INTERMITTENT PORPHYRIA. = EFFETS COMPARATIFS DU GLYCEROL ET DU DEXTROSE SUR L'EXCRETION DES PRECURSEURS PORPHYRINIQUES DANS LA PORPHYRIE AIGUE INTERMITTENTEBONKOWSKY HL; MAGNUSSEN CR; COLLINS AR et al.1976; METABOLISM; U.S.A.; DA. 1976; VOL. 25; NO 4; PP. 405-414; BIBL. 22 REF.Article

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